Dab tsi yog Childhood Interstitial Lung Disease?

Cov txheej txheem:

Dab tsi yog Childhood Interstitial Lung Disease?
Dab tsi yog Childhood Interstitial Lung Disease?
Anonim

Cov kab mob ntsws me me hauv nruab nrab, hu ua "chILD," yog ib pawg ntawm cov mob ntsws tsis tshua muaj tshwm sim uas cuam tshuam rau menyuam mos, menyuam yaus, thiab cov hluas.

Txhua hom menyuam yaus ua rau tus menyuam lub ntsws puas tsuaj, yog li lawv ua haujlwm tsis zoo.

Ntau hom chILD cuam tshuam rau interstitium, cov ntaub so ntswg nyias ntawm cov hnab pa me me thiab cov hlab ntsha hauv lub ntsws. Qee hom menyuam yaus koom nrog lwm qhov chaw hauv lub ntsws, thiab.

Cov kws kho mob nyuam qhuav pib nkag siab txog tus mob no ob peb xyoos dhau los, thiab muaj ntau yam lawv tsis paub. Piv txwv li, lawv tsis paub meej tias muaj pes tsawg tus menyuam muaj menyuam.

Ntawm cov menyuam uas muaj menyuam yaus, qee leej yug nrog nws thiab lwm tus muaj tom qab thaum yau. Cov neeg laus tuaj yeem kis kab mob ntsws interstitial, ib yam nkaus, tab sis qhov ua rau thiab qhov tshwm sim feem ntau txawv.

Caus

Me nyuam yaus tuaj yeem cog tau yam tsis paub qhov laj thawj. Ntawm qhov tod tes, qee yam noob caj noob ces, co toxins, lossis lwm yam kab mob tuaj yeem yog tus neeg ua txhaum.

Qee yam ua tau yog:

Txoj kev mob tshwm sim: Cov kab mob uas ua rau muaj teeb meem nrog surfactant - kua dej hauv lub ntsws uas pab koj tus menyuam ua pa - tuaj yeem kis tau los ntawm cov noob.

Immune system disorders: Qee yam teeb meem ntawm lub cev tiv thaiv kab mob ua rau cov menyuam yaus sib ntaus sib tua.

kab mob autoimmune: Cov no tshwm sim thaum koj tus menyuam lub cev tiv thaiv kab mob ua yuam kev ua rau cov ntaub so ntswg noj qab haus huv. Kab mob plab hnyuv thiab kab mob collagen vascular yog ob yam kab mob autoimmune feem ntau txuas rau chILD.

Kab mob: Qee tus menyuam yaus kis tau tus menyuam tom qab tus mob khaub thuas lossis kab mob.

Kev yug me nyuam tsis xws luag: Cov menyuam mos tuaj yeem yug los muaj qhov tsis zoo thaum yug los ua teeb meem nrog lawv lub ntsws.

Aspiration: Thaum koj nqus zaub mov, kua, lossis ntuav rau hauv koj lub ntsws, kev puas tsuaj tuaj yeem tshwm sim. Kev nqhis dej feem ntau cuam tshuam rau cov menyuam yaus uas muaj teeb meem nqos lossis mob hu ua gastroesophageal reflux disease (GERD).

kev kho mob qog noj ntshav: Kev kho, xws li hluav taws xob thiab tshuaj tua kab mob, tuaj yeem ua rau tus menyuam.

Ib puag ncig ua rau: Tshuaj thiab pwm tuaj yeem ua rau koj tus menyuam lub ntsws ua rau.

Kev phais: Kev hloov lub ntsws lossis hloov cov pob txha pob txha tuaj yeem raug liam rau qee kis ntawm tus menyuam.

Type

Muaj ntau hom menyuam yaus. Muaj ntau lub npe ntev, nyuaj-rau-hais lus. Txawm hais tias lawv txhua tus raug suav hais tias yog kab mob tsawg, qee hom muaj ntau dua hauv cov hnub nyoog tshwj xeeb.

Cov kab mob me me uas feem ntau cuam tshuam rau menyuam mos yog:

  • Surfactant dysfunction mutations
  • Kev txhim kho tsis zoo, xws li alveolar capillary dysplasia
  • mob ntsws loj hlob txawv txav
  • Neuroendocrine cell hyperplasia ntawm me nyuam mos (NEHI)
  • Pulmonary interstitial glycogenosis (PIG)

Hom menyuam yaus uas muaj ntau dua hauv cov menyuam yaus thiab cov hluas yog:

Idiopathic interstitial pneumonias: Cov pawg no suav nrog cryptogenic koom ua mob ntsws, mob ntsws interstitial, tsis muaj mob ntsws, mob ntsws tsis sib xws, thiab lymphocytic interstitial pneumonia

Lwm yam kab mob tseem ceeb: Cov kab mob no tuaj yeem yog alveolar hemorrhage syndromes, aspiration syndromes, hypersensitivity pneumonitis, bronchiolitis obliterans, eosinophilic pneumonia, pulmonary alveolar proteinosis, pulmonary pulmonary infiltrates kab mob (lymphangiomatosis, lymphangiectasis), los yog pulmonary vascular disorders (haemangiomatosis).

ILD-koom nrog cov txheej txheem kab mob: Piv txwv yog cov kab mob sib txuas, kab mob histiocytosis, kab mob qog nqaij hlav, kab mob sarcoidosis, thiab kab mob cia.

Cov kab mob ntawm lub cev tiv thaiv kab mob: Cov pab pawg no suav nrog kev kis tus kab mob kis tau zoo, cov kab mob cuam tshuam txog kev kho mob, lub ntsws thiab cov pob txha pob txha hloov pauv cov kab mob hauv lub ntsws, thiab nthuav tawm cov kab mob alveolar uas tsis paub txog. vim.

Symptoms

Cov tsos mob thiab cov tsos mob ntawm tus me nyuam feem ntau nyob ntawm hom kab mob thiab nws hnyav npaum li cas. Tej zaum lawv yuav muaj xws li:

  • ua pa nyuaj lossis ua tsis taus pa
  • Ua pa nrawm lossis nrov nrov
  • Nyob zoo ib tsoom niam txiv kwv tij neej tsas sawv daws.

  • hnoos lossis mob hauv siab
  • Rov ua mob ntsws ntsws lossis mob ntsws ntsws
  • qis qis qis
  • Tsis hnyav lossis nce siab

Tus Neeg Laus vs. Tus Menyuam Sib Nrauj Kab Mob

Qee tus me nyuam uas tau tus me nyuam yuav muaj mob thoob plaws hauv lawv lub neej, yog li nws muaj peev xwm tshwm sim rau cov menyuam yaus thiab cov laus.

Tab sis thaum tus neeg laus raug kuaj pom tias muaj kab mob ntsws interstitial, cov kws kho mob feem ntau xav tias nws yog ib qho mob txawv kiag li tus me nyuam.

Cov menyuam yaus yuav tsum mus ntsib kws kho mob pulmonologist, tsis yog kws kho mob tshwj xeeb rau cov neeg laus.

Diagnosis

Nws nyuaj rau kuaj tus menyuam. Txhua hom sib txawv, yog li txoj kev uas koj tus kws kho mob siv yuav sib txawv.

Kev kuaj uas pab kuaj tus menyuam muaj xws li:

Chest X-ray lossis CT scan: Cov txheej txheem thaij duab no siv X-ray los thaij duab ntawm koj tus menyuam lub ntsws.

Lung function tests: Cov kws kho mob ntsuas seb cov me nyuam ua pa hauv thiab tawm los kuaj seb lawv lub ntsws ua haujlwm zoo li cas.

Kev kuaj ntshav: Qee zaum cov ntshav rub tau siv los kuaj xyuas cov noob txawv txav.

Bronchoalveolar lavage: Nrog rau txoj kev no, tus kws kho mob txhaj dej ntsev los ntawm lub raj hauv koj tus menyuam lub ntsws kom pom cov hlwb tshwj xeeb. Nws tuaj yeem pab pom qhov raug mob ntawm lub ntsws, kev ua pa, kev kis kab mob, lossis teeb meem ua pa.

Lung biopsy: Tus kws phais tshem tawm ib daim me me ntawm lub ntsws mus kuaj hauv ib lub chaw kuaj.

Kev kho mob

Kev tshawb fawb me me tau ua tiav txog kev kho tus menyuam. Tab sis qee qhov kev kho mob tuaj yeem pab cov me nyuam lub ntsws ua haujlwm zoo dua, yooj yim cov tsos mob, lossis tsuas yog ua rau lawv zoo dua.

Koj tus kws kho mob yuav pom zoo:

Tshuaj: Cov tshuaj steroids txo qis ntsws mob, tshuaj tua kab mob kho kab mob, thiab cov tshuaj bronchodilators pab so cov leeg nqaij ncig ntawm txoj hlab ntsws.

Oxygen: Ntau cov pa tuaj yeem pab cov menyuam ua pa zoo dua thiab ua rau lawv lub siab so.

Khoom noj khoom haus: Kev npaj noj mov uas tsom rau qhov hnyav nce tuaj yeem muaj txiaj ntsig rau qee tus menyuam yaus.

Pulmonary rehab and exercises: Cov kev kho tshwj xeeb yog tsom kom yooj yim rau kev txhaws thiab txhim kho lub ntsws ua haujlwm zoo npaum li cas (koj tus kws kho mob hu qhov no "lub ntsws ua haujlwm").

tshuab ua pa: Cov cuab yeej hu ua lub tshuab ua pa tuaj yeem pab cov menyuam ua pa yooj yim dua.

Kev hloov lub ntsws: Qhov no yuav yog ib qho kev xaiv rau cov menyuam yaus uas muaj mob hnyav lossis ua rau muaj kev phom sij rau lub neej. Txog tam sim no, tus me nyuam zoo li tsis rov qab los rau cov menyuam yaus uas tau phais.

Dab tsi yog Outlook?

Tsis muaj kev kho mob rau tus menyuam, tus mob tshwm sim thiab nce qib sib txawv hauv txhua tus menyuam.

Qee qhov mob hnyav thiab zoo li yuav ua rau muaj kev phom sij rau lub neej thaum ntxov. Lwm hom nyob twj ywm tib yam lossis ua rau qeeb qeeb. Tab sis qee hom kab mob, xws li neuroendocrine cell hyperplasia ntawm cov menyuam mos, tuaj yeem txhim kho lub sijhawm.

Cov menyuam yaus uas muaj menyuam yaus yuav muaj kev xav tau tshwj xeeb. Nws yog ib lub tswv yim zoo los tham nrog cov kws qhia ntawv, cov neeg hauv tsev neeg, thiab lwm tus niam txiv txog txoj hauv kev los txhawb koj tus menyuam thiab koj tsev neeg. Ua tib zoo saib xyuas koj tus kheej noj qab haus huv thiab. Cov neeg saib xyuas feem ntau tso lawv tus kheej kawg, tab sis koj yuav tsum ua tib zoo pab koj tsev neeg.

Pom zoo:

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